FUCA1 Antibody

Size : 50 µL Clone Number: Aliases: Alpha L fucosidase I antibody; Alpha L fucoside fucohydrolase antibody; Alpha-L-fucosidase 1 antibody; Alpha-L-fucosidase I antibody; Alpha-L-fucoside fucohydrolase 1 antibody; FUCA antibody; FUCA1 antibody; FUCO_HUMAN antibody; fucosidase; alpha-L; tissue antibody; fucosidase; alpha-L- 1; tissue antibody; Tissue alpha L fucosidase antibody; Tissue alpha-L-fucosidase antibody Product Type: Polyclonal Antibody Immunogen Species: Homo sapiens (Human) UniProt ID: P04066 Immunogen: Fusion protein of Human FUCA1 Host: Rabbit Reactivity: Human, Mouse Tested Applications: ELISA, WB, IHC; ELISA: 1: 2000-1: 5000, WB: 1: 500-1: 2000, IHC: 1: 50-1: 200 Background: The protein encoded by this gene is a lysosomal enzyme involved in the degradation of fucose-containing glycoproteins and glycolipids. Mutations in this gene are associated with fucosidosis (FUCA1D), which is an autosomal recessive lysosomal storage disease. A pseudogene of this locus is present on chr 2. Clonality: Polyclonal Isotype: IgG Purification Method: Antigen affinity purification Conjugate: Non-conjugated Buffer: -20°C, pH7.4 PBS, 0.05% NaN3, 40% Glycerol Form: Liquid Stroage: Upon receipt, store at -20°C or -80°C. Avoid repeated freeze. Target Names: FUCA1 Research Areas: Metabolism;Signal transduction